Excel File Text File All mouse models of dilated cardiomyopathy with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      dilated cardiomyopathy Cap2tm1e(EUCOMM)Wtsi/Cap2tm1e(EUCOMM)Wtsi C57BL/6N-Cap2tm1e(EUCOMM)Wtsi J:226742 View
dilated cardiomyopathy Ppp3r1tm1.1Jhon/Ppp3r1tm1.1Jhon involves: C57BL/6 * C57BL/6NTac J:298603 View
dilated cardiomyopathy Sod2tm1Shs/Sod2tm1Shs
Tg(Ckmm-cre)5Khn/0
involves: FVB J:171017 View
dilated cardiomyopathy 1A Lmnatm1Gbon/Lmnatm1Gbon involves: 129S2/SvPas * C57BL/6 J:187399 View
dilated cardiomyopathy 1A Lmnatm1Stw/Lmnatm1Stw involves: 129S1/Sv J:87613, J:131905 View
dilated cardiomyopathy 1A Lmnatm2.1Gbon/Lmna+ involves: 129 * C57BL/6 J:198526 View
dilated cardiomyopathy 1A Lmnatm3Stw/Lmnatm3Stw involves: 129S1/Sv * 129S4/SvJaeSor * C57BL J:100393 View
dilated cardiomyopathy 1C Ldb3tm4Chen/Ldb3tm4Chen
A1cfTg(Myh6-cre/Esr1*)1Jmk/A1cf+
involves: 129S1/Sv * 129X1/SvJ * Black Swiss * FVB/N J:144739 View
dilated cardiomyopathy 1C Ldb3tm4Chen/Ldb3tm4Chen
Myl2tm1(cre)Krc/Myl2+
involves: 129S1/Sv * 129S4/SvJae * 129X1/SvJ * Black Swiss J:144739 View
dilated cardiomyopathy 1CC Nexnem1Chen/Nexnem1Chen C57BL/6J-Nexnem1Chen J:301807 View
dilated cardiomyopathy 1CC Nexntm1.1Chen/Nexntm1.1Chen Not Specified J:290931 View
dilated cardiomyopathy 1CC Nexntm1Chen/Nexntm1Chen
Tg(myl7.L-cre)1118Tmhn/0
involves: MF1 J:290931 View
dilated cardiomyopathy 1CC Nexntm1Chen/Nexntm1Chen
Tg(Tnnt2-cre)5Blh/0
involves: C57BL/6 * DBA/2 J:290931 View
dilated cardiomyopathy 1D Tnnt2tm2.1Feah/Tnnt2+ involves: 129S6/SvEvTac * FVB/N J:243725 View
dilated cardiomyopathy 1D Tnnt2tm2Mmto/Tnnt2+ involves: 129S/SvEv * C57BL/6 J:137784 View
dilated cardiomyopathy 1D Tnnt2tm2Mmto/Tnnt2tm2Mmto involves: 129S/SvEv * C57BL/6 J:137784 View
dilated cardiomyopathy 1DD Rbm20em1Hgra/Rbm20+ C57BL/6-Rbm20em1Hgra J:324088 View
dilated cardiomyopathy 1DD Rbm20em1Hgra/Rbm20em1Hgra C57BL/6-Rbm20em1Hgra J:324088 View
dilated cardiomyopathy 1DD Rbm20em1Hide/Rbm20em1Hide involves: C57BL/6J J:297234 View
dilated cardiomyopathy 1EE Myh6tm2Ces/Myh6+ involves: 129S/SvEv * 129X1/SvJ J:114549 View
dilated cardiomyopathy 1EE Myh6tm2Ces/Myh6tm2Ces involves: 129S/SvEv * 129X1/SvJ J:114549 View
dilated cardiomyopathy 1G Ttntm1Brge/Ttn+ B6.Cg-Ttntm1Brge J:152736 View
dilated cardiomyopathy 1HH Bag3tm1c(EUCOMM)Hmgu/Bag3tm1.1Chen
Tg(Myhca-cre)1Abel/0
involves: 129S1/Sv * 129X1/SvJ * C57BL/6J * C57BL/6N * FVB/N J:246352 View
dilated cardiomyopathy 1HH Bag3tm1c(EUCOMM)Hmgu/Bag3tm1c(EUCOMM)Hmgu
Tg(Myhca-cre)1Abel/0
involves: C57BL/6N * FVB/N J:246352 View
dilated cardiomyopathy 1I Destm1Cap/Destm1Cap involves: 129S7/SvEvBrd * C57BL/6 J:35123 View
dilated cardiomyopathy 1L Sgcdtm1Kcam/Sgcdtm1Kcam involves: 129S1/Sv * 129X1/SvJ J:57107 View
dilated cardiomyopathy 1L Sgcdtm1Mcn/Sgcdtm1Mcn B6.129-Sgcdtm1Mcn/J J:234761 View
dilated cardiomyopathy 1L Sgcdtm1Mcn/Sgcdtm1Mcn involves: 129S1/Sv * 129T2/SvEmsJ * 129X1/SvJ J:76730 View
dilated cardiomyopathy 1L Sgcdtm1Ojml/Sgcd+ B6.129-Sgcdtm1Ojml J:234761 View
dilated cardiomyopathy 1M Csrp3tm1Crni/Csrp3tm1Crni Not Specified J:38213 View
dilated cardiomyopathy 2F Bag5em1Asay/Bag5em1Asay C57BL/6JJcl-Bag5em1Asay J:327046 View
      dilated cardiomyopathy b2b904.1Clo/b2b904.1Clo C57BL/6J-b2b904.1Clo J:175213 View
dilated cardiomyopathy b2b904Clo/b2b904Clo C57BL/6J-b2b904Clo J:175213 View
dilated cardiomyopathy Cenpftm1Dbdr/Cenpftm1Dbdr
Tg(Tnnt2-cre)5Blh/0
involves: C57BL/6 * DBA/2 * ICR J:185133 View
dilated cardiomyopathy Cox7a1tm1Hutt/Cox7a1tm1Hutt B6.129-Cox7a1tm1Hutt J:192141 View
dilated cardiomyopathy Ctsltm1Cptr/Ctsltm1Cptr involves: 129P2/OlaHsd J:76333 View
dilated cardiomyopathy Dag1tm2Kcam/Dag1tm2Kcam
Myl2tm1(cre)Krc/Myl2+
involves: 129S1/Sv * 129S4/SvJae * 129X1/SvJ J:169951 View
dilated cardiomyopathy Dicer1tm1Smr/Dicer1tm1Smr
Tg(Myh6-cre)2182Mds/0
involves: 129S7/SvEvBrd * FVB/N J:131962 View
dilated cardiomyopathy Dnm1lPy/Dnm1l+ involves: BALB/cAnNCrl * C3H/HeH J:161510 View
dilated cardiomyopathy Erbb2tm1Cbm/Erbb2tm2Cbm
Myl2tm1(cre)Krc/Myl2+
involves: 129P2/OlaHsd * 129S4/SvJae J:77347 View
dilated cardiomyopathy Esrrbtm1.1Nat/Esrrbtm1.1Nat
Tg(Myh6-cre)2182Mds/0
involves: 129S6/SvEvTac * C57BL/6 * C57BL/6N * FVB/N J:241078 View
dilated cardiomyopathy Ilktm1Star/Ilktm1Star
Tg(Ckmm-cre)1Lrsn/0
involves: 129S1/Sv * 129X1/SvJ * FVB/N J:112174 View
dilated cardiomyopathy Lmod2Tn(pb-Act-RFP)1.1Zhu/Lmod2Tn(pb-Act-RFP)1.1Zhu involves: FVB/N J:233669 View
dilated cardiomyopathy Lrrc10tm1Sgt/Lrrc10tm1Sgt B6.129P2-Lrrc10tm1Sgt J:195548 View
dilated cardiomyopathy Mdm4tm2Glo/Mdm4tm2.1Glo
Tg(Myh6-cre)2182Mds/0
involves: 129S4/SvJaeSor * 129S7/SvEvBrd * C57BL/6J * FVB/N J:137114 View
dilated cardiomyopathy Med1tm2Jkr/Med1tm2Jkr
A1cfTg(Myh6-cre/Esr1*)1Jmk/A1cf+
involves: 129P2/OlaHsd * FVB/N J:243730 View
dilated cardiomyopathy Med1tm2Jkr/Med1tm2Jkr
Tg(Myh6-cre)2182Mds/0
involves: 129P2/OlaHsd * FVB/N J:243730 View
dilated cardiomyopathy Mrgprdtm5Mjz/Mrgprdtm5Mjz B6.129S1-Mrgprdtm5Mjz/Mmnc J:269603 View
dilated cardiomyopathy Mtif3tm1c(EUCOMM)Wtsi/Mtif3tm1c(EUCOMM)Wtsi
Tg(Ckmm-cre)5Khn/0
involves: C57BL/6N J:287609 View
dilated cardiomyopathy Myh6tm1Ces/Myh6+ involves: 129S/SvEv * 129X1/SvJ J:114549 View
dilated cardiomyopathy Myh6tm1Ces/Myh6tm1Ces involves: 129S/SvEv * 129X1/SvJ J:114549 View
dilated cardiomyopathy Myocdtm1Msp/Myocdtm1Msp
A1cfTg(Myh6-cre/Esr1*)1Jmk/A1cf+
involves: 129/Sv * C57BL/6J * FVB/N J:154666 View
dilated cardiomyopathy Myocdtm1Msp/Myocdtm1Msp
Tg(Myh6-cre)2182Mds/0
involves: 129/Sv * FVB/N J:154666 View
dilated cardiomyopathy Ncoa6tm1Jkr/Ncoa6+
Tg(Myh6-cre)2182Mds/0
involves: 129P2/OlaHsd * FVB/N J:269856 View
dilated cardiomyopathy Ncoa6tm1Jkr/Ncoa6tm1Jkr
Tg(Myh6-cre)2182Mds/0
involves: 129P2/OlaHsd * FVB/N J:269856 View
dilated cardiomyopathy Pdcd1tm1Hon/Pdcd1tm1Hon C.129S2(B6)-Pdcd1tm1Hon J:66979 View
dilated cardiomyopathy Pdlim5tm1.1Chen/Pdlim5tm1.1Chen involves: 129S1/Sv * 129X1/SvJ * Black Swiss J:175042 View
dilated cardiomyopathy Pdlim5tm1Chen/Pdlim5tm1Chen
Tg(Tnnt2-cre)5Blh/?
involves: 129S1/Sv * 129X1/SvJ * Black Swiss * C57BL/6 * DBA/2 J:175042 View
dilated cardiomyopathy Prox1tm2Gco/Prox1tm2Gco
Nkx2-5tm1(cre)Rjs/Nkx2-5+
involves: 129S1/Sv * 129S7/SvEvBrd J:212185 View
dilated cardiomyopathy Ptger4tm1.1Matb/Ptger4tm1.1Matb
Tg(Myh6-cre)2182Mds/0
involves: 129S6/SvEvTac * FVB/N J:158439 View
dilated cardiomyopathy Ptpn11tm1Gsf/Ptpn11tm1Gsf
Tg(Ckmm-cre)5Khn/0
involves: 129S1/Sv * 129X1/SvJ * FVB J:144767 View
dilated cardiomyopathy Rbm24tm1.1Xixu/Rbm24tm1.1Xixu
Tg(Myh6-cre)1Xya/0
involves: C57BL/6NTac J:302917 View
dilated cardiomyopathy Rtf1tm1c(KOMP)Wtsi/Rtf1tm1c(KOMP)Wtsi
A1cfTg(Myh6-cre/Esr1*)1Jmk/A1cf+
involves: C57BL/6N * FVB/N J:338311 View
dilated cardiomyopathy Sdhaf4em1Bcgen/Sdhaf4em1Bcgen
Tg(Ckmm-cre)5Khn/0
B6.Cg-Sdhaf4em1Bcgen Tg(Ckmm-cre)5Khn J:345348 View
dilated cardiomyopathy Srftm1Zli/Srftm1Zli
A1cfTg(Myh6-cre/Esr1*)1Jmk/A1cf+
involves: 129 * C57BL/6J * FVB/N J:135043 View
dilated cardiomyopathy Tbx20tm1.1Rph/Tbx20+ involves: C57BL/6 J:98489 View
dilated cardiomyopathy Timp3tm1Rkho/Timp3tm1Rkho B6.129-Timp3tm1Rkho J:102205 View
dilated cardiomyopathy Timp3tm1Rkho/Timp3tm1Rkho involves: 129 * C57BL/6 J:112033 View
dilated cardiomyopathy Yme1l1tm1Tlan/Yme1l1tm1Tlan
Tg(Myh6-cre)2182Mds/0
involves: C57BL/6 * C57BL/6NCrl * FVB/N J:229455 View
dilated cardiomyopathy 1A Dot1ltm1Tche/Dot1ltm1.1Tche
Tg(Myhca-cre)1Abel/0
Not Specified J:168140 View
peripartum cardiomyopathy Stat3tm1Vpo/Stat3tm1Vpo
Tg(Myh6-cre)2182Mds/0
involves: 129P2/OlaHsd * FVB/N J:141591 View
X-linked dilated cardiomyopathy Xlch/? C57BL/6J-Xlch J:136798 View
X-linked dilated cardiomyopathy Xlch/Xlch+ involves: C3H/HeJ * C57BL/6J J:136798 View
      dilated cardiomyopathy 1E Scn5atm1(SCN5A)Rdn/Scn5atm3(SCN5A*)Rdn involves: 129S6/SvEvTac J:189389 View
dilated cardiomyopathy 1E Scn5atm3(SCN5A*)Rdn/Scn5atm3(SCN5A*)Rdn involves: 129S6/SvEvTac J:189389 View
dilated cardiomyopathy 1P Tg(Myh6-Pln*R9C)#Ces/0 involves: FVB/N J:82353 View
dilated cardiomyopathy 1R Tg(Myh6-Actc1*R312H)307Iko/? involves: C57BL/6 J:178587 View
dilated cardiomyopathy 1Y Tg(Myh6-Tpm1*E54K)30Dfw/0 involves: FVB/N J:137813 View
dilated cardiomyopathy 1Y Tg(Myh6-Tpm1*E54K)67Dfw/0 involves: FVB/N J:137813 View
Transgenes and
Other Mutations
     dilated cardiomyopathy A1cfTg(Myh6-cre/Esr1*)1Jmk/A1cf+
Tg(Myh6-2A)#Know/0
involves: BALB/c * C57BL/6 * FVB/N J:128060 View
dilated cardiomyopathy Tg(CAG-Ncoa6)87Hwl/0 involves: FVB J:269856 View
dilated cardiomyopathy Tg(CAMalpha1b)7Wjk/? Not Specified J:134704 View
dilated cardiomyopathy Tg(MT2A-TGFBR2)#Rser/0 involves: C57BL/6 * DBA J:158480 View
dilated cardiomyopathy Tg(Myh6-BRUNOL4*)10Coop/0 involves: FVB J:99369 View
dilated cardiomyopathy Tg(Myh6-Camk2d_ic)LJhb/0 either: (involves: Black Swiss) or (involves: C57BL/6) J:130644 View
dilated cardiomyopathy Tg(Myh6-Camk2d_ic)MJhb/0 either: (involves: Black Swiss) or (involves: C57BL/6) J:130644 View
dilated cardiomyopathy Tg(Myh6-CASQ2)1Mord/0 Not Specified J:79838 View
dilated cardiomyopathy Tg(Myh6-cre)TG9Pjay/0 involves: FVB/N J:119070 View
dilated cardiomyopathy Tg(Myh6-CREB1*S133A)1Jml/0 involves: CD-1 J:133881 View
dilated cardiomyopathy Tg(Myh6-EGFR*)9-12Iko/0 involves: C57BL/6 * DBA/2 J:182337 View
dilated cardiomyopathy Tg(Myh6-Gnaq*Q209L)44Ejne/0 involves: FVB J:127756 View
dilated cardiomyopathy Tg(Myh6-Gnaq*Q209L)44Ejne/Tg(Myh6-Gnaq*Q209L)44Ejne involves: FVB J:127756 View
dilated cardiomyopathy Tg(Myh6-Gnaq*Q209L)52Ejne/? involves: FVB J:204274 View
dilated cardiomyopathy Tg(Myh6-HBEGF)#Iko/0 involves: C57BL/6 * DBA/2 J:93335 View
dilated cardiomyopathy Tg(Myh6-MYL2*D94A)1Dsc/0 Not Specified J:258888 View
dilated cardiomyopathy Tg(Myh6-NEBL*A592E)#Jato/0 Not Specified J:242962 View
dilated cardiomyopathy Tg(Myh6-NEBL*G202R)#Jato/0 Not Specified J:242962 View
dilated cardiomyopathy Tg(Myh6-Ppp3ca)37Eno/0 involves: FVB J:93176 View
dilated cardiomyopathy Tg(Myh6-Prkaca)2Eno/0 Not Specified J:263774 View
dilated cardiomyopathy Tg(Myh6-Prkaca)33Eno/0 Not Specified J:263774 View
dilated cardiomyopathy Tg(Myh6-PRKCE*A159E)344Robo/? involves: FVB J:198401 View
dilated cardiomyopathy Tg(Myh6-Rab1a)highGwd/0 involves: FVB/N J:134581 View
dilated cardiomyopathy Tg(Myh6-Rab1a)lowGwd/0 involves: FVB/N J:134581 View
dilated cardiomyopathy Tg(Myh6-Rab1a)medGwd/0 involves: FVB/N J:134581 View
dilated cardiomyopathy Tg(Myh6-Rest*)474Ysai/0 involves: C57BL/6J J:86837 View
dilated cardiomyopathy Tg(Myh6-Rxra)41Pcn/0 Not Specified J:60351 View
dilated cardiomyopathy Tg(Myh6-Snai1)B10Jcc/0 Not Specified J:126850 View
dilated cardiomyopathy Tg(Myh6-Snai1)B10Jcc/Tg(Myh6-Snai1)B10Jcc Not Specified J:126850 View
dilated cardiomyopathy Tg(Myh6-STK4)28Jusa/0 involves: C57BL/6 J:139414 View
dilated cardiomyopathy Tg(Myh6-Tmod1)65Msus/Tg(Myh6-Tmod1)65Msus FVB/N-Tg(Myh6-Tmod1)65Msus J:58879 View
dilated cardiomyopathy Tg(Myh6-Tmod1)65Msus/Tg(Myh6-Tmod1)65Msus involves: FVB/N J:107823 View
dilated cardiomyopathy Tg(Myh6-Tnf)1.6Amf/0 involves: FVB J:104759 View
dilated cardiomyopathy Tg(Myh6-Tnni3*)1Ammu/0 involves: A/J * C57BL/6 J:104770 View
dilated cardiomyopathy Tg(Myh6-tTA)6Smbf/0
Tg(tetO-Spp1)5Gad/0
involves: C57BL/6 * CBA J:194810 View
dilated cardiomyopathy Tg(Myh6-tTA)6Smbf/0
Tg(tetORo1-lacZ)3Conk/0
FVB.Cg-Tg(Myh6-tTA)6Smbf Tg(tetORo1-lacZ)3Conk J:107363 View
dilated cardiomyopathy Tg(Myh7-Phc1)#Yota/0 involves: C57BL/6 J:75968 View
dilated cardiomyopathy Tg(Myh7-RARA/lacZ)30Mcco/0 Not Specified J:146424 View
dilated cardiomyopathy 1A Tg(Myh6-LMNA*E82K)35Lizh/0 involves: C57BL/6J J:167734 View
dilated cardiomyopathy 1C Tg(Myh6-LDB3*S196L)93Mva/0 involves: C57BL/6J J:243711 View
dilated cardiomyopathy 1D Tg(Myh6-TNNT2*R141W)#Ajm/0 involves: C3H * C57BL/6 * ICR J:161899 View
dilated cardiomyopathy 1D Tg(Myh6-TNNT2*R141W)#Lian/0 involves: C57BL/6J J:211769 View
dilated cardiomyopathy 1E Tg(Myh6-rtTA)8585Jam/0
Tg(Myh6*/tetO-SCN5A*F1759A)#Marx/0
involves: C57BL/6 * CBA * FVB/NTac J:229825 View
dilated cardiomyopathy 1L Tg(Myh6-Sgcd*S151A)5Mcn/0 involves: 129T2/SvEms * C57BL/6J J:117855 View
dilated cardiomyopathy 1P Tg(Myh6-Pln*)#Egk/0 Not Specified J:105976 View
dilated cardiomyopathy 1R Tg(Myh6-ACTC1*E361G)361.20Sbm/0 Not Specified J:242344 View
dilated cardiomyopathy 1Y Tg(Myh6-Tpm1*D230N)HJcf/0 B6.FVB-Tg(Myh6-Tpm1*D230N)HJcf J:243724 View
Additional
Complex
Models
     dilated cardiomyopathy Gt(ROSA)26Sortm1(CAG-Nr2f2)Tsa/Gt(ROSA)26Sor+
A1cfTg(Myh6-cre/Esr1*)1Jmk/A1cf+
involves: 129S1/Sv * 129X1/SvJ * FVB/N J:227012 View
dilated cardiomyopathy Jundtm1Mya/Jundtm1Mya
Tg(H2-K-Fosl1)1Wag/0
involves: 129S2/SvPas * C57BL/6 * CBA J:95691 View
dilated cardiomyopathy 1A H2-Ab1b-tm1Gru/H2-Ab1b-tm1Gru
Tg(CD2-CD4,HLA-DQA1,HLA-DQB1)1Ell/Tg(CD2-CD4,HLA-DQA1,HLA-DQB1)1Ell
NOD.Cg-H2-Ab1b-tm1Gru Tg(CD2-CD4,HLA-DQA1,HLA-DQB1)1Ell J:86540 View


       
No similarity to the expected human disease phenotype was found.
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
NOT Models      dilated cardiomyopathy 1D Tnnt2tm1Mmto/Tnnt2+ involves: 129S/SvEv J:141967 View