Excel File Text File All mouse models of mitochondrial complex I deficiency with phenotypic similarity to the human disease
        Disease Term Allelic Composition Genetic Background Reference Phenotypes
      nuclear type mitochondrial complex I deficiency 20 Acad9tm1c(KOMP)Wtsi/Acad9tm1c(KOMP)Wtsi
Tg(ACTA1-cre)79Jme/0
involves: C57BL/6J * C57BL/6N * FVB/N * SJL J:326969 View
nuclear type mitochondrial complex I deficiency 20 Acad9tm1c(KOMP)Wtsi/Acad9tm1c(KOMP)Wtsi
Tg(Myh6-cre)2182Mds/0
involves: C57BL/6N * FVB/N J:326969 View
      mitochondrial complex I deficiency Aifm1Hq/Aifm1Hq B6CBACa Aw-J/A-Aifm1Hq/J J:144096 View
mitochondrial complex I deficiency Aifm1Hq/Y B6CBACa Aw-J/A-Aifm1Hq/J J:144096 View
mitochondrial complex I deficiency Ndufa1tm1.1Nay/Ndufa1tm1.1Nay involves: 129S1/SvImJ * 129S4/SvJaeSor * 129S6/SvEvTac J:257477 View
mitochondrial complex I deficiency Ndufs4tm1Capt/Ndufs4+ involves: 129S6/SvEvTac * C57BL/6NTac J:192154 View
mitochondrial complex I deficiency Ndufs6Gt(AR0138)Wtsi/Ndufs6Gt(AR0138)Wtsi involves: 129P2/OlaHsd * C57BL/6 J:183619 View